... the intravenous infusion of analogue exceeds 10 min-1 kg-1 and does not appear to be secondary to changes in urine flow or sodium excretion. 3. A mechanism for induced basic amino- aciduria conditions is suggested. Key words: amino acid analogues, basic amino acid transport, cystinuria, lysinuria. Abbreviations...

...Tomoaki Kato 1. The effect of intravenous infusion of l-lysine and l-arginine on the tubular reabsorption of dibasic amino acids and cystine was studied in normal individuals and in homozygous and heterozygous subjects with cystinuria. 2. The control subjects reabsorbed almost all filtered lysine...

...A. D. Stephens; D. Perrett 1. A family is reported with an unusual type of cystinuria. 2. The propositus presented with a cystine renal stone; the renal tubular reabsorption of cystine was grossly abnormal but the tubular reabsorption of ornithine, lysine and arginine was only slightly less than...

...D. B. A. Silk; D. Perrett; A. D. Stephens; M. L. Clark; E. F. Scowen 1. An intestinal perfusion technique has been used to study absorption in vivo of l-cystine and l-cysteine in six normal human subjects and three patients with homozygous cystinuria. 2. No significant absorption of l-cystine...

... reabsorption of amino acids in health and disease, the presence of homoarginine and its excessive loss in cystinuria must be accounted for. 28 6 1973 © 1974 The Biochemical Society and the Medical Research Society 1974 cystinuria renal tubular transport inborn errors of amino acid...

..., have been determined in three normal adults, five homozygous cystinuric patients, and three persons, two ‘completely’ and the third ‘incompletely’ recessive, heterozygotes for cystinuria. All the cystinuric patients were found to have thresholds at less than 1 mg of lysine/100 ml of plasma...

... confirm the existence of dipeptide transport systems independent of those for free amino acids. 25 4 1972 © 1972 The Biochemical Society and the Medical Research Society 1972 amino acid transport dipeptide transport cystinuria Clinical Science (1972) 43,659-668. INTESTINAL DIPEPTIDE...